Entropion,ectropion, ptosis

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Eyelid musclesEyelid muscles

THE EYELID MUSCLESTHE EYELID MUSCLES

How the lids are kept in placeHow the lids are kept in place

Eyelid musclesEyelid muscles

The palpebral fissureThe palpebral fissure

Why do the eyelids not fall outwards?Why do the eyelids not fall outwards?

Why do the eyelids not turn inwards? Why do the eyelids not turn inwards?

How is the fissure width maintained?How is the fissure width maintained?

Eyelid musclesEyelid muscles

The palpebral fissureThe palpebral fissure

Why are they apposed to the globe –just so?Why are they apposed to the globe –just so?

TARSUS - CANTHAL LIGAMENTS – BONETARSUS - CANTHAL LIGAMENTS – BONE

Eyelid musclesEyelid muscles

The palpebral fissureThe palpebral fissure

Superior and inferior tarsusSuperior and inferior tarsusMedial and lateral canthal ligamentsMedial and lateral canthal ligaments

Lacrimal crests and lateral orbital tubercleLacrimal crests and lateral orbital tubercle

Eyelid musclesEyelid muscles

Horizontal lid laxityHorizontal lid laxity

Laxity of canthal ligamentsLaxity of canthal ligaments With gravity – With gravity – ectropionectropion With lid retractor laxity - With lid retractor laxity - entropionentropion

Eyelid musclesEyelid muscles

The palpebral fissureThe palpebral fissure

What keeps the upper lid up and the What keeps the upper lid up and the

lower lid down?lower lid down?THE EYELID RETRACTORS

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Upper lid retractorsUpper lid retractorsLevator aponeurosisLevator aponeurosisSuperior tarsal muscle (Muller’s)Superior tarsal muscle (Muller’s)

Lower lid retractorsLower lid retractorsCapsulopalpebral fasciaCapsulopalpebral fasciaInferior tarsal muscleInferior tarsal muscle

Orbital septum fuses with the retractorsOrbital septum fuses with the retractors

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Levator aponeurosisLevator aponeurosis Wide insertion Wide insertion Various layers of eyelidVarious layers of eyelid

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Levator aponeurosisLevator aponeurosisInsertionsInsertions1.1. Medial horn – posterior Medial horn – posterior

lacrimal crestlacrimal crest2.2. Lateral horn – lateral Lateral horn – lateral

orbital tubercleorbital tubercle3.3. Anterior portion – skinAnterior portion – skin4.4. Posterior portion – Posterior portion –

anterior tarsusanterior tarsus5.5. ConjunctivaConjunctiva

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Muller’s muscleMuller’s muscle

(superior tarsal muscle)(superior tarsal muscle) Posterior part of levatorPosterior part of levator 2 mm lift to the upper lid2 mm lift to the upper lid Insertion to tarsus and Insertion to tarsus and

conjunctivaconjunctiva Sympathetic supplySympathetic supply Horner’s syndrome – mild Horner’s syndrome – mild

ptosisptosis

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Lower lid retractor Lower lid retractor Capsulopalpebral fasciaCapsulopalpebral fascia From inferior rectus From inferior rectus

terminal fibresterminal fibres Encircles inferior Encircles inferior

oblique oblique Inserts to inferior Inserts to inferior

conjunctival fornix and conjunctival fornix and inferior tarsal border inferior tarsal border

Eyelid musclesEyelid muscles

Eyelid retractorsEyelid retractors

Upper lid retractorsUpper lid retractorsrarefactionrarefactiondisinsertion disinsertion PTOSISPTOSISdehiscencedehiscence

Lower lid retractorsLower lid retractors ECTROPIONECTROPIONattenuationattenuation ENTROPIONENTROPION

Eyelid musclesEyelid muscles

Result from imbalance between forces on Result from imbalance between forces on anterior and posterior lamellaeanterior and posterior lamellae

Ectropion - EntropionEctropion - Entropion

Eyelid musclesEyelid muscles

Ectropion - EntropionEctropion - Entropion

Initiator of imbalance – horizontal lid laxity

Tarsal instability

Gravity

Ectropion Entropion

lower lid retractor weakness

Eyelid musclesEyelid muscles

Outward turning of eyelid marginOutward turning of eyelid margin

TypesTypes

1.1. CongenitalCongenital

2.2. InvolutionalInvolutional

3.3. ParalyticParalytic

4.4. CicatricialCicatricial

5.5. MechanicalMechanical

EctropionEctropion

Eyelid musclesEyelid muscles

Most common type in practiceMost common type in practiceInvolutionalInvolutional

Primary etiologic factorPrimary etiologic factorHorizontal eyelid laxityHorizontal eyelid laxity

Clinical testClinical testThe snap testThe snap test

EctropionEctropion

Eyelid musclesEyelid muscles

Testing lid laxityTesting lid laxity

EctropionEctropion

Eyelid musclesEyelid muscles

Involutional ectropionInvolutional ectropionLower lidLower lidEpiphoraEpiphoraConjunctival Conjunctival

hypertrophyhypertrophyKeratinisationKeratinisation

EctropionEctropion

Eyelid musclesEyelid muscles

Paralytic ectropionParalytic ectropion

EctropionEctropion

Facial palsy

Eyelid musclesEyelid muscles

Cicatricial ectropionCicatricial ectropion

EctropionEctropion

Eyelid musclesEyelid muscles

Mechanical ectropionMechanical ectropion

EctropionEctropion

Eyelid musclesEyelid muscles

Inversion of eyelid marginInversion of eyelid margin

TypesTypes

1.1. CongenitalCongenital

2.2. Acute spasticAcute spastic

3.3. InvolutionalInvolutional

4.4. CicatricialCicatricial

Lower lid involutional entropion is Lower lid involutional entropion is

more common more common

EntropionEntropion

Eyelid musclesEyelid muscles

Involutional entropionInvolutional entropion

EntropionEntropion

Eyelid musclesEyelid muscles

Involutional entropionInvolutional entropion

EntropionEntropion

Eyelid musclesEyelid muscles

Results inResults in EpiphoraEpiphora Corneal abrasionsCorneal abrasions Corneal vascularizationCorneal vascularization

EntropionEntropion

Eyelid musclesEyelid muscles

MedialMedial

conjunctivoplasty/conjunctivoplasty/

Medial spindle Medial spindle

procedureprocedure

Ectropion surgeryEctropion surgery

Lateral canthoplasty/Lateral tarsal

strip procedure

Eyelid musclesEyelid muscles

Lazy-T procedureLazy-T procedure

MedialMedial

ConjunctivoplastyConjunctivoplasty

++

Full thickness Full thickness

excisionexcision

Ectropion surgeryEctropion surgery

Eyelid musclesEyelid muscles

Modified Modified

Kuhnt-Szymanowski Kuhnt-Szymanowski

procedureprocedure

Ectropion SurgeryEctropion Surgery

Eyelid musclesEyelid muscles

Transverse Transverse

lid everting suturelid everting suture

Entropion surgeryEntropion surgery

Eyelid musclesEyelid muscles

Weis procedureWeis procedure

Lid splitting Lid splitting

+ +

marginal rotationmarginal rotation

Entropion surgeryEntropion surgery

Eyelid musclesEyelid muscles

What is ptosis?What is ptosis?

It is an abnormally low It is an abnormally low position of the upper lid position of the upper lid

Eyelid musclesEyelid muscles

PtosisPtosis

How to How to diagnosediagnose mild ptosis? mild ptosis?What has What has causedcaused it? it?What is the What is the degreedegree of ptosis? of ptosis? Is it an indicator of a Is it an indicator of a seriousserious

disease?disease?How to choose the right How to choose the right

surgery surgery ??

Eyelid musclesEyelid muscles

PtosisPtosis

DiagnosisDiagnosisDrooping > 2 mm of cornea Drooping > 2 mm of cornea

coveredcoveredFrontalis overaction – forehead Frontalis overaction – forehead

wrinkleswrinklesChin elevation in bilateral ptosisChin elevation in bilateral ptosisRule out pseudoptosisRule out pseudoptosis

Eyelid musclesEyelid muscles

PtosisPtosis

Chin elevationChin elevation

Eyelid musclesEyelid muscles

PtosisPtosis

Brow elevationBrow elevation

Eyelid musclesEyelid muscles

PtosisPtosis

What has caused it?What has caused it?

ClassificationClassification• Congenital / AcquiredCongenital / Acquired• Lesion at the level ofLesion at the level of

nervenerve

musclemuscle

aponeurosisaponeurosis

Eyelid musclesEyelid muscles

PtosisPtosis

EtiologyEtiology

1.1. MyogenicMyogenic

2.2. AponeuroticAponeurotic

3.3. NeurogenicNeurogenic

4.4. MechanicalMechanical

5.5. TraumaticTraumatic

Eyelid musclesEyelid muscles

PtosisPtosis

MMost common acquired ptosisost common acquired ptosis

AponeuroticAponeurotic

MMost common congenital ptosisost common congenital ptosis

MyogenicMyogenic

Eyelid musclesEyelid muscles

PtosisPtosis

Congenital myogenic ptosisCongenital myogenic ptosis

Eyelid musclesEyelid muscles

PtosisPtosis

Aponeurotic ptosisAponeurotic ptosis

Eyelid musclesEyelid muscles

PtosisPtosis

Paralytic ptosisParalytic ptosis

Eyelid musclesEyelid muscles

PtosisPtosis

Mechanical ptosisMechanical ptosis

NeurofibromatosisNeurofibromatosis

Eyelid musclesEyelid muscles

PtosisPtosis

AAponeurotic ptosisponeurotic ptosis

InvolutionalInvolutional

PostoperativePostoperative

MechanismMechanism

rarefactionrarefaction

disinsertiondisinsertion

dehiscencedehiscence

Eyelid musclesEyelid muscles

PtosisPtosis

AAponeurotic ptosisponeurotic ptosis aging / surgeryaging / surgery high upper lid creasehigh upper lid crease

normal – 8-10 mmnormal – 8-10 mm

levator attachments to skinlevator attachments to skin

thinning of lidthinning of lid near normalnear normal levator functionlevator function

Eyelid musclesEyelid muscles

PtosisPtosis

AAponeurotic ptosisponeurotic ptosis

Brow elevation, high crease,

deep sulcus, thinned lid

Eyelid musclesEyelid muscles

PtosisPtosisCCongenital ptosisongenital ptosisSimpleSimple developmental dystrophy of developmental dystrophy of

levator musclelevator muscle Absent / weak lid creaseAbsent / weak lid crease reduced levator functionreduced levator function

Eyelid musclesEyelid muscles

PtosisPtosis

CCongenital ptosisongenital ptosis

SimpleSimple lid lag in downgazelid lag in downgaze weakness of superior rectus weakness of superior rectus

+/-+/- amblyopia from amblyopia from

astigmatismastigmatism

anisometropiaanisometropia

occlusionocclusion

Eyelid musclesEyelid muscles

PtosisPtosis

CCongenital ptosisongenital ptosis

Obscuring visual axis

Eyelid musclesEyelid muscles

PtosisPtosis

Marcus Gunn jaw-winking syndromeMarcus Gunn jaw-winking syndrome

CCongenital ptosisongenital ptosis

Eyelid musclesEyelid muscles

PtosisPtosis

Congenital Congenital

MyogenicMyogenic

Mild to severeMild to severe

ptosisptosis

Acquired Acquired

AponeuroticAponeurotic

Mild to severeMild to severe

ptosisptosis

PalpebralPalpebral

fissure heightfissure height

Eyelid musclesEyelid muscles

PtosisPtosis

Congenital Congenital

MyogenicMyogenic

Weak orWeak or

absentabsent

Acquired Acquired

AponeuroticAponeurotic

Higher thanHigher than

normalnormal

Upper eyelidUpper eyelid

CreaseCrease

Eyelid musclesEyelid muscles

PtosisPtosis

Congenital Congenital

MyogenicMyogenic

ReducedReduced

Acquired Acquired

AponeuroticAponeurotic

Near normalNear normalLevatorLevator

functionfunction

Eyelid musclesEyelid muscles

PtosisPtosis

Congenital Congenital

MyogenicMyogenic

Eyelid lagEyelid lag

Acquired Acquired

AponeuroticAponeurotic

Eyelid dropEyelid dropOn downgazeOn downgaze

Eyelid musclesEyelid muscles

PtosisPtosis

AsAs an indicator of a serious disorder an indicator of a serious disorder

Myasthenia gravisMyasthenia gravis ocular involvement in 90%ocular involvement in 90% presenting feature in 60%presenting feature in 60% variable ptosis, bilateral, variable ptosis, bilateral,

asymmetricasymmetric worsens towards eveningworsens towards evening Tensilon testing Tensilon testing

Eyelid musclesEyelid muscles

PtosisPtosis

AsAs an indicator of a serious disorder an indicator of a serious disorder Myasthenia gravisMyasthenia gravis

Ptosis RE Ptosis LE, 3 months later

Eyelid musclesEyelid muscles

PtosisPtosis

AsAs an indicator of a serious disorder an indicator of a serious disorder

Neurogenic ptosisNeurogenic ptosis oculomotor nerve palsyoculomotor nerve palsy

diabetes / diabetes / hypertensionhypertension

intracranial intracranial aneurysmsaneurysms

/ tumors / trauma/ tumors / trauma check for III nerve functionscheck for III nerve functions

Eyelid musclesEyelid muscles

PtosisPtosis

Pancoast’sPancoast’s tumor / carotid aneurysms / malignant tumor / carotid aneurysms / malignant cervical lymph nodes cervical lymph nodes

Horner’s syndrome

before cocaine after cocaine

Eyelid musclesEyelid muscles

PtosisPtosis

AsAs an indicator of a serious disorder an indicator of a serious disorder

NNeurogenic ptosiseurogenic ptosis• Oculosympathetic palsyOculosympathetic palsy

(Horner’s syndrome)(Horner’s syndrome) mild ptosis as a rulemild ptosis as a rule miosismiosis normal pupillary reactionsnormal pupillary reactions Pancoast’s tumor / carotid Pancoast’s tumor / carotid

aneurysms / malignant cervical aneurysms / malignant cervical lymph nodeslymph nodes

Eyelid musclesEyelid muscles

PtosisPtosis

DDegree of ptosisegree of ptosis

MeasurementsMeasurements• Palpebral fissure heightPalpebral fissure height• Margin reflex distanceMargin reflex distance• Upper eyelid creaseUpper eyelid crease• Levator functionLevator function

Eyelid musclesEyelid muscles

PtosisPtosis

DDegree of ptosisegree of ptosis

MeasurementsMeasurements

Poor levator function

Eyelid musclesEyelid muscles

PtosisPtosis

DDegree of ptosisegree of ptosis

MeasurementsMeasurements

Ptosis data sheet

Eyelid musclesEyelid muscles

PtosisPtosis

DDegree of ptosisegree of ptosis

MeasurementsMeasurements

Amount PtosisAmount Ptosis ClassificationClassification

less than or equal to 2mmless than or equal to 2mm MildMild

3mm3mm ModerateModerate

greater than or equal to 4mmgreater than or equal to 4mm SevereSevere

Amount of droop from normal

Eyelid musclesEyelid muscles

PtosisPtosis

DDegree of ptosisegree of ptosis

MeasurementsMeasurements

Levator function

Levator Muscle ExcursionLevator Muscle Excursion ClassificationClassification

15mm15mm NormalNormal

greater than or equal to 8mmgreater than or equal to 8mm GoodGood

5-7mm5-7mm FairFair

less than or equal to 4mmless than or equal to 4mm PoorPoor

Eyelid musclesEyelid muscles

PtosisPtosis

AAdditional testsdditional testsOcular motilityOcular motilityLid in downgazeLid in downgazeAmblyopia Amblyopia Bell’s phenomenonBell’s phenomenonPharmacologic testingPharmacologic testing

Eyelid musclesEyelid muscles

PtosisPtosis

SSurgeryurgery

Dependent on levator functionDependent on levator function

Normal function

Levator aponeurosis advancement / reinsertion

Eyelid musclesEyelid muscles

PtosisPtosis

SSurgeryurgeryDependent on levator functionDependent on levator functionFor mild ptosisFor mild ptosis

Mild ptosisHorner’s

Fasanella-Servat procedure(tarsoconjunctival)Muller’s muscle resection

Eyelid musclesEyelid muscles

PtosisPtosisSSurgeryurgery

Dependent on levator functionDependent on levator function

Moderate tosevere ptosis

Levator resection Amount of resection according to degree of ptosis

Eyelid musclesEyelid muscles

PtosisPtosis

SSurgeryurgery

Dependent on levator functionDependent on levator function

Absent function

Frontalis suspensionAutogenous fascia lata or synthetic materials

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