Sarkoma Ewing

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EWINGS SARCOMA:

EWINGS SARCOMA:Rare, young, 10-20 years, Males 2:1Lesion at Diaphysis of long bones, pelvis, femur dan tibiaHistopath : sheets uniform round cells phleomorphic cytoplasmic glycogen, extensive necrosis; 11/22 translocation

Ewings Sarcoma:

Ewings: uniform round clear cells.Nyeri dengan tumor jaringan lunak disekitarnya Demam :

Leucositosis ; anemia ; ESR Mirip osteomyelitis ( DD )Dx. Biopsi, X-Ray, MRITx. Chemoterapi : reseksiMetastase ; survival rate rendah Prognosis: Sangat buruk,