58
F.R.C.S.(Eng.), F.R.C.S.(Tr.& Orth.) Professor of Orthopaedics Giant Aneurysmal Bone Cyst 3/3/2013 1 Professor Freih Abuhassan - University of Jordan

Giant bone cysts - البروفيسور فريح ابوحسان - استشاري اورام العظام في الاردن

Embed Size (px)

Citation preview

F.R.C.S.(Eng.), F.R.C.S.(Tr.& Orth.)

Professor of Orthopaedics

Giant Aneurysmal Bone Cyst

3/3/2013 1 Professor Freih Abuhassan - University

of Jordan

Patient profile: A 9-years old male child, MF, Overweight.

Chief complaint:

Progressive painless swelling of the right distal thigh of 14 m duration

Referred to us on the

17th Nov. 2008 3/3/2013 2

Professor Freih Abuhassan - University

of Jordan

History of present illness:

4th Sep. 2007, had pain in the distal femur after a fall while playing.

Diagnosed as pathological fracture of the distal femur.

3/3/2013 3 Professor Freih Abuhassan - University

of Jordan

4th Sep. 2007

3/3/2013 4 Professor Freih Abuhassan - University

of Jordan

Treated by complete POP for 3 M

4th Dec. 2007

3/3/2013 5 Professor Freih Abuhassan - University

of Jordan

19th Jan. 2008

Trivial trauma Supracondylar distal

femur fractures treated by POP for

7 weeks

3/3/2013 6 Professor Freih Abuhassan - University

of Jordan

19th Jan. 2008 3/3/2013 7

Professor Freih Abuhassan - University

of Jordan

5th Mar. 2008 3/3/2013 8

Professor Freih Abuhassan - University

of Jordan

Past medical history

=History of two surgical biopsies with

blood transfusion

Diagnosis: Aneurysmal bone cyst

3/3/2013 9 Professor Freih Abuhassan - University

of Jordan

Patient offered the following

advices outside JUH

1- Above Knee Amputation

2- Resection and Joint replacement

3- To be treated abroad

Patient was wheel chair dependent

since the start of treatment. 3/3/2013 10

Professor Freih Abuhassan - University

of Jordan

6th June 2008

Lesion contineued to grow

3/3/2013 11

Professor Freih Abuhassan - University

of Jordan

26th Sep. 2008

3/3/2013 12 Professor Freih Abuhassan - University

of Jordan

Physical examination:

General: no abnormality detected

Right lower limb:

= Diffuse swelling of the knee and lower thigh with

10 cm diameter difference form the left thigh

(firm, not tender, not pulsatile)

=Decreased knee ROM due to the bulky swelling

=Normal distal NV examination

17th Nov. 2008

3/3/2013 13 Professor Freih Abuhassan - University

of Jordan

3/3/2013 14 Professor Freih Abuhassan - University

of Jordan

3/3/2013 15 Professor Freih Abuhassan - University

of Jordan

3/3/2013 16 Professor Freih Abuhassan - University

of Jordan

Laboratory investigation

CBC

KFT

LFT

ESR

CRP

All were Normal

3/3/2013 17 Professor Freih Abuhassan - University

of Jordan

17th Nov. 2008

3/3/2013 18 Professor Freih Abuhassan - University

of Jordan

3/3/2013 19 Professor Freih Abuhassan - University

of Jordan

3/3/2013 20 Professor Freih Abuhassan - University

of Jordan

3/3/2013 21 Professor Freih Abuhassan - University

of Jordan

3/3/2013 22 Professor Freih Abuhassan - University

of Jordan

3/3/2013 23 Professor Freih Abuhassan - University

of Jordan

Surgery at JUH

19th Nov. 2008

Local curretage of the cyst +

application of monoplanar external

fixator + Circular Ex.Fix. (across

the knee joint) Ilizarov Frame.

First stage

3/3/2013 24 Professor Freih Abuhassan - University

of Jordan

Problems 1- Difficult to apply Tourniquet

2- Lateral Scar of previous surgery

3-Soft bone (prolonged disuse)

4-Extensive bleeding

5-Overweight

6-Residual defect after resection.

3/3/2013 25

Professor Freih Abuhassan - University

of Jordan

Histopathology

ABC 3/3/2013 26

Professor Freih Abuhassan - University

of Jordan

3/3/2013 27 Professor Freih Abuhassan -

University of Jordan

3/3/2013 28 Professor Freih Abuhassan -

University of Jordan

3/3/2013 29 Professor Freih Abuhassan -

University of Jordan

3/3/2013 30 Professor Freih Abuhassan -

University of Jordan

= Under tourniquet, Anterior approach,

Complete resection of the cyst.

=Turbid hematoma was found inside

the cavity.

=Delay reconstruction of the bone

defect till results of C&S.

=Bone cement spacer was inserted.

16th Dec. 2008 2nd stage Surgery

3/3/2013 31 Professor Freih Abuhassan - University

of Jordan

3/3/2013 32 Professor Freih Abuhassan -

University of Jordan

3/3/2013 33 Professor Freih Abuhassan -

University of Jordan

Bone cement spacer

Cultures: no bacterial growth

Gram stain:

only WBC’s & RBC’s, no bacteria

3/3/2013 34 Professor Freih Abuhassan - University

of Jordan

Reconstructive Procedure

3/3/2013 35 Professor Freih Abuhassan - University

of Jordan

3nd stage Surgery

23rd Dec. 2008 1. Removal of Cement spacer

2. Strut tibial autograft from the mid

ipsilateral tibia, to femur and

stabilized by long screws to the

ilizarov frame.

3. Application of ilizarov to tibia +

bone marrow inserted.

3/3/2013 36 Professor Freih Abuhassan - University

of Jordan

3/3/2013 37 Professor Freih Abuhassan - University

of Jordan

3/3/2013 38 Professor Freih Abuhassan - University

of Jordan

3/3/2013 39 Professor Freih Abuhassan - University

of Jordan

Periosteal closure

3/3/2013 40 Professor Freih Abuhassan -

University of Jordan

Bone marrow injection

23rd Dec. 2008 3/3/2013 41

Professor Freih Abuhassan -

University of Jordan

3/3/2013 42 Professor Freih Abuhassan - University

of Jordan

3/3/2013 43 Professor Freih Abuhassan - University

of Jordan

5th Jan. 2009

Admitted as a case popliteal fossa

swelling to R/O organised hematoma

U/S: no definite fluid collection but

significant soft tissue edema.

= Percutaneous evacuation of hematoma,

=R/O Orthofix and application of long

Ilizarov plate externally and fixed to the

graft by Schanz screws 3/3/2013 44

Professor Freih Abuhassan - University

of Jordan

Followed regularly in OPD

Partial weight bearing was started

in the on 21st Jan. 2009.

Now FWB on crutches

3/3/2013 45 Professor Freih Abuhassan - University

of Jordan

25th March 2009

3/3/2013 46 Professor Freih Abuhassan -

University of Jordan

3/3/2013 47 Professor Freih Abuhassan -

University of Jordan

With Ilizarov family

3/3/2013 48 Professor Freih Abuhassan -

University of Jordan

ABC In 1942, Jaffe and Lichtenstein

first described ABC when they

discovered "a peculiar blood

containing cyst of large size.

3/3/2013 49 Professor Freih Abuhassan - University

of Jordan

Benign Aggressive Bone Tumor

Locally destructive yet do not

metastasize or show malignant

changes at a cellular levelcellular

level

ABC, GCT, CMF,

Chondroblastoma,

Osteoblastoma. 3/3/2013 50

Professor Freih Abuhassan - University

of Jordan

WHO

Blood-filled spaces of variable

size,separated by CT containing

trabeculae of bone or osteoid

tissue and osteoclast giant cells

ABCs represent 1%–2% of all

primary bone lesions

3/3/2013 51 Professor Freih Abuhassan - University

of Jordan

Giant Cell tumour

Aneurysmal bone cyst

Telangiectatic osteosarcoma

Secondary ABC –upto 35% of all ABCs

Most commonly due to GCT (39%)

D.Dx

3/3/2013 52 Professor Freih Abuhassan - University

of Jordan

No bone is immune

3/3/2013 53

Giant Humerus ABC

3/3/2013 54 Professor Freih Abuhassan -

University of Jordan

Giant femur ABC

3/3/2013 55 Professor Freih Abuhassan - University

of Jordan

Giant ABCs

3/3/2013 56 Professor Freih Abuhassan -

University of Jordan

Local recurrence rate after

classic surgical procedures

(curettage and grafting) is about

11.8%–30.8%

Treatment depends on

site & size of the lesion.

3/3/2013 57 Professor Freih Abuhassan - University

of Jordan

3/3/2013 58 Professor Freih Abuhassan - University

of Jordan