IMAGING DEPARTMENT

Jan 24th, 2012 Reported by Dr. Le Giang

Name: Doan Thi Tuyet Nhung Sex: Female Age: 4 y Dept: Outpatient

Clinical

Visual disturbance Headache

MRI findingsT2WI, Axial

Suprasellar & intrasellar mass (22x24x34 mm) Mixed component: cystic & solid part

(calcification) Displacement of chiasm

MRI findingsT1WI, Sagital

Sellar enlargement ( AP: 21mm) , hardly compress pituitary Heterogenous intensity (iso & hypo signal) calcification &

fluid Cystic contents hyperintense to cerebrospinal fluid

MRI findingsT1WI, Coronal

Cyst content hyperintense to CSF

MRI findingsT1WI, Axial, Post C+

Solid portion enhance heterogenously Cyst wall strong enhances Circle of Willis encased by mass

MRI findingsT1WI, Post C+

Compress hardly pituitary

MRI findingsT1WI, Post C+

Solid portion enhance heterogenously Cyst wall strong enhances

Diagnosis

CRANIOPHARYNGIOMA

Background

CrP is slow- growing & benign tumor. Histologically benign epithelial tumor arising from squamous rests

along involuted hypophyseal-Rathke duct. 2 Types: Adamentinomatous & Papillary 6-9% of all Ped intracranial tumors. Location: Suprasellar (75%), Supra & intrasellar ( 21%), Intrasellar

(4%). Age: Peak at 8-12 y. Imaging findings: Cystic supracellar mass with calcification &

enhancement of a mural nodule of cyst wall. Displacement of chiasm.

90% are cystic; 90% have calcification; 90% enhancement cyst wall

Treatment: surgical & radiation therapy. Prognosis: 64-96% overall 10 years survival 20% recurrence rate if <5cm 80% recurrence rate if> 5cm Can recur up to 30 years after resection.

Thank you for attention!