Pediatric Nursing9(Gastrointestinal Disorder)

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    Pediatric NursingGastrointestinal

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    Function

    1. Assists in maintaining F&E and acid1. Assists in maintaining F&E and acid--base balancebase balance

    2. Processes and absorbs nutrients to2. Processes and absorbs nutrients tomaintain metabolism and supportmaintain metabolism and supportgrowth and developmentgrowth and development

    3.Ex

    crete waste products from3.Ex

    crete waste products fromdigestive processdigestive process

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    Recommended DailyAllowance

    Calories: 120 cal/Kbw/day; 360Calories: 120 cal/Kbw/day; 360--380 cal380 caldailydaily

    ProteinProtein 2.2 g/Kbw/day2.2 g/Kbw/day FluidsFluids 1616--20 cc/kg/day20 cc/kg/day

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    Supplementary Feeding

    Supplementary feedingSupplementary feeding 44--6 months6 months

    Never wean an infant if inNever wean an infant if in

    1.Solid foods in order:1.Solid foods in order: -- cerealscereals rich in ironrich in iron

    -- fruitsfruits

    -- vegetablesvegetables

    -- meatmeat

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    2. begin in small quantities2. begin in small quantities

    3.Finger foods3.Finger foods offered at 6 monthsoffered at 6 months

    4.Soft table foods4.Soft table foods 1 year1 year 5. Dilute fruit juices5. Dilute fruit juices 6 months; 1 is to6 months; 1 is to

    4 ounces of water4 ounces of water

    6. Never give half cooked eggs6. Never give half cooked eggs salmonelliosis/gastroenteritissalmonelliosis/gastroenteritis

    7. Dont give honey7. Dont give honey infant botulisminfant botulism

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    8. Offer food one at a time8. Offer food one at a time interval ofinterval of44--7 days7 days

    Total body fluidsTotal body fluids 6565--85% of body85% of bodyweightweight

    Greater in extracellularGreater in extracellular dehydrationdehydration

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    Acid-Base Balance

    1.Chemical buffers1.Chemical buffers

    2.Renal and respiratory system2.Renal and respiratory system

    3. Dilution of strong acids and bases in blood3. Dilution of strong acids and bases in blood Respiratory acidosisRespiratory acidosis carbonic acid excesscarbonic acid excess

    -- hypoventilationhypoventilation

    -- RDSRDS

    -- COPDCOPD

    -- LaryngotracheobronchitisLaryngotracheobronchitis

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    Respiratory alkalosisRespiratory alkalosis carbonic acidcarbonic aciddeficitdeficit

    -- hyperventilationhyperventilation -- feverfever

    -- encephalopathyencephalopathy

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    etabolic acidosisMetabolic acidosis base HCO3 deficitbase HCO3 deficit

    -- diarrheadiarrhea

    -- severe dehydrationsevere dehydration -- malnutritionmalnutrition

    -- ciliac crisisciliac crisis

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    Metabolic alkalosisMetabolic alkalosis case HCO3 excesscase HCO3 excess

    -- uncontrolled vomitinguncontrolled vomiting

    -- NGT insertionNGT insertion -- gastric lavagegastric lavage

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    Problems Leading to F&EImbalance

    1. Vomiting1. Vomiting forceful expulsion offorceful expulsion ofstomach contentsstomach contents

    Sx:Sx: NauseaNausea

    DizzinessDizziness

    Facial flushingFacial flushingAbdominal crampingAbdominal cramping

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    Assess:Assess:

    AmountAmount

    FrequencyFrequency ForceForce projectileprojectile

    Mgt:Mgt:

    BRAT dietBRAT diet banana, rice, apply sauce,banana, rice, apply sauce,toasttoast

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    Diarrhea

    Exaggerated excretion of intestinalExaggerated excretion of intestinalcontentscontents

    Types:Types: 1. Acute1. Acute related to gastroenteritis,related to gastroenteritis,

    salmonellasissalmonellasis

    -- dietary indescretiondietary indescretion -- antibiotic use (Ampicillin, tetracycline)antibiotic use (Ampicillin, tetracycline)

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    2.Chronic non2.Chronic non--specificspecific

    Cause:Cause:

    1. food intolerance1. food intolerance 2.Excessive fluid intake2.Excessive fluid intake

    3. carbohydrate and protein3. carbohydrate and proteinmalabsorptionmalabsorption

    Assess:Assess:

    Frequency, consistency, appearanceFrequency, consistency, appearance

    Best criteria: consistencyBest criteria: consistency

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    Complication:Complication:

    DehydrationDehydration

    MildMild 5% wt loss5% wt loss ModerateModerate 10% wt loss10% wt loss

    SeverSever 15% wt loss15% wt loss

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    Early signs and symptoms:Early signs and symptoms:

    Tachycardia, tachypnea, hypotensionTachycardia, tachypnea, hypotension

    Increase temp, sunken fontanel andIncrease temp, sunken fontanel andeyeballs, absence of tearseyeballs, absence of tears

    Weight loss, scanty urine, dry skinWeight loss, scanty urine, dry skin

    Severe dehydration: marked oliguria,Severe dehydration: marked oliguria,prolonged capillary refillprolonged capillary refill

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    Mgt:Mgt:

    Acute:Acute:

    -- NPONPO -- IV therapyIV therapy

    -- prone to hypokalemiaprone to hypokalemia

    DrugDrug NaHCO3NaHCO3

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    Chronic:Chronic:

    -- thickened feeding with baby cerealsthickened feeding with baby cereals

    -- feed slowly, burp often (every 1feed slowly, burp often (every 1ounce)ounce)

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    Hirschprungss Disease

    Congenital aganglionic megacolonCongenital aganglionic megacolon

    Earliest sign:Earliest sign:

    1. failure to pass meconium after 241. failure to pass meconium after 24hourshours

    2. abdominal distention2. abdominal distention

    3. vomitus of fecal material3. vomitus of fecal material 4. foul smelling breath4. foul smelling breath

    Early childhoodEarly childhood ribbonribbon--like stoollike stool

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    Diagnosis

    1. Barium enema1. Barium enema reveals narrowedreveals narrowedportion of bowelportion of bowel

    2.Rectal biopsy2.Rectal biopsy reveals absence ofreveals absence ofaganglionic cellsaganglionic cells

    3. Abdominal X3. Abdominal X--rayray reveals dilatedreveals dilated

    loops on intestineloops on intestine 4.Rectal manometry4.Rectal manometry reveals failurereveals failure

    of intestine sphincter to relaxof intestine sphincter to relax

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    Management

    1. NGT feeding1. NGT feeding

    2.Surgery2.Surgery

    -- Temporary colostomyTemporary colostomy -- anastomosis and pull throughanastomosis and pull through

    porcedureporcedure

    DietDiet increase protein, increaseincrease protein, increasecalories, decrease residuecalories, decrease residue pastapasta

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    Gastroesophageal Reflux Disease

    AchalasiaAchalasia

    Regurgitation of stomach contents intoRegurgitation of stomach contents into

    the esophagusthe esophagus ComplicationComplication esophagitis; aspirationesophagitis; aspiration

    pneumoniapneumonia

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    Management

    AnticholinergicAnticholinergic

    1. Betanicol (Urecholine)1. Betanicol (Urecholine) increaseincrease

    esophageal tone and peristaltic activityesophageal tone and peristaltic activity 2. Metachlorpromide (Reglam)2. Metachlorpromide (Reglam)

    decrease esophageal pressure bydecrease esophageal pressure by

    relaxing pyloric duodenal segmentsrelaxing pyloric duodenal segments

    -- increase peristalsis withoutincrease peristalsis withoutstimulating secretionsstimulating secretions

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    3. H2 Receptor Antagonist3. H2 Receptor Antagonist decreasedecreasegastric acidity and pepsin secretiongastric acidity and pepsin secretion

    -- Ranitidine (Zantac)Ranitidine (Zantac)AntacidAntacid neutralizes gastric acidneutralizes gastric acid

    between feedingsbetween feedings

    -- MaaloxMaalox SurgerySurgery Nissen funduplicationNissen funduplication

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    Esophageal Cancer

    Assessment:Assessment:

    1.Chronic vomiting1.Chronic vomiting

    2.Failure to thrive syndrome2.Failure to thrive syndrome 4. Melena or hematemesis4. Melena or hematemesis

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    Diagnosis

    1.Esophagoscopy1.Esophagoscopy

    2.Esophageal manometry2.Esophageal manometry relvealsrelveals

    lower esophageal sphincter pressurelower esophageal sphincter pressure 3. Intra esophageal pH content3. Intra esophageal pH content

    reveals pH of distal esophagusreveals pH of distal esophagus

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    Pyloric Stenosis

    Hypertrophy of muscles of pylorusHypertrophy of muscles of pyloruscausing narrowing and obstructioncausing narrowing and obstruction

    Outstanding signOutstanding sign projectile vomitingprojectile vomiting -- vomitingvomiting initial sign of upper GIinitial sign of upper GI

    obstructionobstruction

    -- vomitus of upper GIvomitus of upper GI blood tingedblood tinged -- vomitus of lower GIvomitus of lower GI bile streaked;bile streaked;

    bilousbilous

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    -- abdominal distentionabdominal distention major sign ofmajor sign oflower GI obstructionlower GI obstruction

    Metabolic alkalosisMetabolic alkalosis Failure to gain weightFailure to gain weight

    Olive shaped massOlive shaped mass

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    Diagnosis

    Increase Na and K, decrease ClIncrease Na and K, decrease Cl

    UltrasoundUltrasound

    XX--ray with barium swallowray with barium swallowABGABG

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    Management

    1. Pyloromyotomy1. Pyloromyotomy incision of pyloricincision of pyloricmusclemuscle

    2.Fredt2.Fredt--Ramstedt procedureRamstedt procedure separation of hyperthrophied muscleseparation of hyperthrophied musclewithout incisionwithout incision

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    Intussusception

    Invagination or telescoping of positionInvagination or telescoping of positionof bowel to anotherof bowel to another

    Common site: distal ileum and proximalCommon site: distal ileum and proximalcoloncolon

    Prone: eats fastProne: eats fast

    ComplicationComplication -- peritonitisperitonitis

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    Sn/Sx:Sn/Sx:

    1. persistent paroxysmal abdominal1. persistent paroxysmal abdominal

    painpain severesevere FrequencyFrequency 1515--20 minutes20 minutes

    2. vomiting2. vomiting contains bilecontains bile

    3. currant jelly stool3. currant jelly stool after 12 hoursafter 12 hours 4. sausage4. sausage--shaped massshaped mass

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    Management

    Hydrostatic reduction with bariumHydrostatic reduction with bariumenemaenema

    Pneumatic insufflationPneumatic insufflation airair SurgerySurgery anastomosis and pull throughanastomosis and pull through

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    Inborn Errors of Metabolism

    Phenylketonuria (PKU)Phenylketonuria (PKU)

    Deficiency of liver enzymeDeficiency of liver enzyme

    phenylalanine hydroxylasephenylalanine hydroxylase Prevents conversion of phenylalanine toPrevents conversion of phenylalanine to

    tyrosinetyrosine

    TyrosineTyrosine epinephrine, thyroxine,epinephrine, thyroxine,melaninmelanin

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    Signs and Symptoms

    1. Urine has musty or mousy odor1. Urine has musty or mousy odor phenylpyruvic acidphenylpyruvic acid

    2. Atopic dermatitis2. Atopic dermatitis 3.Seizures3.Seizures

    4. Growth retardation4. Growth retardation -- thyroxinethyroxine

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    Diagnosis

    Guthrie testGuthrie test bacterial inhibitionbacterial inhibition

    Pheric chloridePheric chloride green spots in thegreen spots in the

    diaper as sign of PKUdiaper as sign of PKU

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    Diet

    Low phenylalanine dietLow phenylalanine diet contraindicatecontraindicatehigh protein foodshigh protein foods

    LofenalacLofenalac extremelyextremely--lowlowphenylalanine formulaphenylalanine formula

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    Galactosemia

    Carbohydrate metabolism disorderCarbohydrate metabolism disorder

    Deficient: galactose 1Deficient: galactose 1--phosphatephosphate

    uridyltransferaseuridyltransferase May die at 3 days of ageMay die at 3 days of age

    Symptoms:Symptoms:

    GalactosemiaGalactosemia GalactosuriaGalactosuria

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    Diagnosis

    Beutler testBeutler test screening test; uses cordscreening test; uses cordbloodblood

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    Management

    DietDiet galactosegalactose--freefree

    NutramigenNutramigen milk substitute formulamilk substitute formula

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    Celiac Disease

    GlutenGluten--induced Enteropathyinduced Enteropathy

    Intolerance to:Intolerance to:

    BB barleybarley RR ryerye

    OO oatoat

    WW wheatwheat Inability to absorb fatInability to absorb fat

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    Early sign:Early sign:

    1. Diarrhea1. Diarrhea

    2.Constipation2.Constipation 3. Vomiting3. Vomiting

    Late sign:Late sign:

    1. Abdominal pain1. Abdominal pain protuberantprotuberantabdomenabdomen

    2.Steatorrhea2.Steatorrhea

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    Diagnosis

    1. history and clinical symptoms1. history and clinical symptoms

    2.Serum analysis2.Serum analysis IgA antigliadinIgA antigliadin

    antibodiesantibodies

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    Management

    GlutenGluten--free dietfree diet lifetimelifetime

    Rice and cornRice and corn OKOK

    Vitamin supplementsVitamin supplements Mineral supplementsMineral supplements