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R. SNEKAVALLIROLL NO - 73
INTRODUCTION
LEPROSY - FOREMOST CAUSE OF DEFORMITY & CRIPPLING
25% OF PATIENT - NOT TREATED AT AN EARLY STAGE DEVELOP ANAESTHESIA & DEFORMITIES OF HAND & FEET
THREE TIER CONSEQUENCES OF LEPROSY
IMPAIRMENT
DISABILITYHANDICAP
IMPAIRMENT –ANATOMIC, PHYSIOLOGIC,
PSYCHOLOGIC ABNORMALITIES OR LOSES RESULTING FROM DISEASE OR DISORDERDISABILITY –
IMPAIRMENTS – PROBLEMS – AFFECTED INDIVIDUALS – CERTAIN TASKS & ACTIVITIES – NORMAL FOR PERSONS AGE, SEX, TRAINING – BECOME DIFFICULT OR IMPOSSIBLE
THIS DIFFICULTY – INABILITY – CARRY OUT TASK - DISABILITY
HANDICAP –DISADVANTAGES WHICH MAKE
DISABLED INDIVIDUALS UNABLE TO DISCHARGE THEIR SOCIAL OBLIGATIONS
DEFORMITY & DISABILITY IN LEPROSY
RISK FACTORSTYPE OF LEPROSY DURATION OF ACTIVE DISEASE NUMBER OF NERVE TRUNKS
INVOLVED
THREE KINDS OF DEFORMITIES
DEFORMITY
SPECIFIC PARALYTIC ANAESTHETIC
LOCAL LEPROSY RELATED
PATHOLOGY
COMMON IN FACE
DAMAGE TO MOTOR NERVES
COMMON IN HAND
DAMAGE TO SENSORY NERVES AND LOSS OF
SENSIBILITY
COMMON IN FEET
DEFORMITY MAY BE DUE TO DISEASE PROCESS eg. LOSS OF
EYEBROWS
PERIPHERAL NERVE DAMAGE - PARALYSIS OF MUSCLES eg. CLAW HAND
RESULTING FROM INJURIES TO HAND AND FEET eg. MUTILATION OF HAND & FEET
DEFORMITIES OCCURING IN LEPROSY
NERVE STAGES OF NERVE INVOLVEMENT
STAGE OF PARASITIZATIONSTAGE OF HOST RESPONSESTAGE OF CLINICAL INVOLVEMENTSTAGE OF NERVE DAMAGESTAGE OF NERVE DESTRUCTION
PERIPHERAL NERVES AFFECTED
SUPERFICIALLY LOCATED DERMAL NERVE TWIGS
CUTANEOUS NERVESNERVE TRUNKS LOCATED DEEP TO
THE DEEP FASCIAUPPER LIMB – ULNAR NERVE
THICKENINGLOWER LIMB – COMMON PERONEAL
NERVE
MODES OF ONSET AND PROGRESSQUIET NERVE PARALYSISEPISODIC ONSET & SALTATORY
PROGRESSCATASTROPHIC MODE OF ONSETNERVE DAMAGE OF LATE ONSET
ACUTE NEURITIS – SEVERE PAIN & TENDERNESS
ENL NEURITISNERVE ABSCESS
COLD ABSCESS HOT ABSCESS
CASEOUS NECROSIS OF NERVE FASCICLES
BT,TT
ENL RELATED NEURITIS
FACE MASK FACEFACIES LEONINA
SAGGING FACELOSS OF EYEBROWS (SUPERCILIARY
MADAROSIS)
LOSS OF EYELASHES (CILIARY MADAROSIS)
EYE
CORNEAL ULCERSACUTE IRITISCORNEAL OPACITY
LAGOPTHALMOS
BLINDNESS
EARNODULES ON THE EAR
ELONGATED LOBULESEAR DEFORMITIES
NOSE
PERFORATED NOSEDEPRESSED NOSESUNKEN NOSE DEFROMITY
HANDULNAR CLAW HAND –
ULNAR NERVE INVOLVEMENT
HYPEREXTENSION - METACARPO - PHALANGEAL JOINT & FLEXION -PROXIMAL & THE DISTAL INTER-PHALANGEAL JOINTS
DUE TO PARALYSIS OF LUMBRICALS – SUPPLY BY ULNAR NERVE
WRIST DROP – RADIAL NERVE
PALSY WRIST - PALMAR
FLEXION - WEAKNESS OF DORSIFLEXORS
EXTENSOR MUSCLES OF THE FOREARM AND THE HAND
APE THUMB DEFORMITY -
MEDIAN NERVE PARALYSIS OF
OPPONENS POLLISIS MUSCLE
TOTAL CLAW HAND – ULNAR & MEDIAN NERVE INVOLVEMENT
HOLLOWING OF INTROSSEOUS SPACES & SWOLLEN HAND
FEET
FOOT DROP –COMMON PERONEAL NERVE
INVOLVEMENTPLANTAR FLEXION DUE TO
WEAKNESS OF THE DORSIFLEXORS
FOOT DROP
PLANTAR ULCER -DUE TO NERVE INVOLVEMENT -
ANAESTHESIA
CLAWING OF TOESABSORPTION OF TOESCOLLAPSED FOOTSWOLLEN FOOT AND CALLOSITIES
ABSORPTION OF TOES
OTHER DEFORMITIES
GYNAECOMASTIAPERFORATION OF PALATEACUTE EPIDIDYMO ORCHITIS
GRADING
HANDS & FEET -GRADE 0 - NO ANAESTHESIA & NO
VISIBLE DEFORMITYGRADE 1 – ANAESTHESIA BUT NO
VISIBLE DEFORMITYGRADE 2 – VISIBLE DEFORMITY
DAMAGE PRESENT
GRADING
EYE -GRADE 0 – NO EYE PROBLEM, NO
EVIDENCE OF LOSS OF VISIONGRADE 1 – EYE PROBLEM DUE TO
LEPROSY PRESENT BUT VISION NOT AFFECTED
GRADE 2 – SEVERE VISUAL IMPAIRMENT, LAGOPTHALMOS, IRITIS, CORNEAL OPACITY
INTERVENTIONS
FIRST LEVEL -
Primary, secondary & psychological impairment
Anti-leprosy treatment, health education, supportive social action
SECOND LEVEL –
Reversible disability preventive measures
Early recognition and treatment
THIRD LEVEL –
Permanent irreversible disabilities
Physiotherapy, corrective measures, provision of appliances
FOURTH LEVEL –
Disability & handicap
Rehabilitation measures
FIFTH LEVEL –FOR THE DESTITUTESRESCUE, RESTORE & REHABILITATE
MANAGEMENT
NERVE DAMAGE CAUSES 3 LEVELS OF PROBLEMS – ONE LEADING TO THE NEXT
LEVEL 1 LEVEL 3LEVEL 2
LEVEL 1 LEVEL 2 LEVEL 3
OFTEN OFTEN PREVENTABLE WITH PREVENTABLE WITH
MEDICAL MEDICAL TREATMENT OF TREATMENT OF
LEPROSY BEFORE LEPROSY BEFORE THERE IS NERVE THERE IS NERVE
DAMAGEDAMAGE
OFTEN PREVENTABLE OFTEN PREVENTABLE WITH PROTECTIVE EYE WITH PROTECTIVE EYE
AND SKIN CARE AND AND SKIN CARE AND EXERCISE TO KEEP EXERCISE TO KEEP FULL MOVEMENT OF FULL MOVEMENT OF
JOINTSJOINTS
OFTEN PREVENTABLE OFTEN PREVENTABLE WITH CAREFUL EARLY WITH CAREFUL EARLY
TREATMENT OF SORES, TREATMENT OF SORES, BURNS AND INFECTIONSBURNS AND INFECTIONS
A Person with leprosy gets a
blister
It does not hurt. So keeps walking until blister bursts -
infected
Still without pain - infection Still without pain - infection gets deeper and attacks the gets deeper and attacks the
bonebone
Bone is destroyed - foot becomes Bone is destroyed - foot becomes more and more deformed.more and more deformed.
PREVENTION OF INJURY FOR PERSONS WITH LOSS OF FEELING&
STRENGTHEYE – EYE DAMAGE – COMES FROM NOT
BLINKING ENOUGH, BECAUSE OF WEAKNESS OR LOSS OF FEELING
BLINKING - EYES WET AND CLEAN. PERSON DOES NOT BLINK WELL, OR HIS EYES ARE RED, THEN ADVICE -
TO WEAR SUNGLASSES WITH SIDE SHADES, AND MAY BE SUN HAT
CLOSE EYES TIGHTLY – DAY- ESPECIALLY WHEN DUST BLOWS
ROLL THE EYEBALLS UP AS YOU TRY TO CLOSE EYES TIGHT
KEEP EYES CLEAN. WASH WELL AROUND EYES, KEEP
FLIES AND DIRTY HANDS AWAY
NERVE
ACUTE NEURITIS – ANTI-REACTION THERAPY – STEROIDS & ANALGESICS, SEDATIVES
ENL NEURITIS – THALIDOMIDELOCAL MEASURES – SPLINTING OF
THE PART PHYSICAL THERAPY – WAX BATH,
SHORTWAVE OR MICROWAVE DIATHERMY
SURGICAL DECOMPRESSION OF NERVE TRUNKS
INDICATION - MEDICAL & AUXILLARY TREATMENT
FAILED
PROCEDURE - RELEASE EXTERNAL COMPRESSING
FACTOR DIVIDE EPINEURIUM RELIEVE THE FASCICLES FROM BEING
STRANGULATED BY THE SCLEROSED EPINEURIUM
NERVE ABSCESSCOLD ABSCESS – SURGICAL
INTERVENTION – DRAINING THE ABSCESS – MOPPING – NECROTIC CONTENT – REMOVING ADHERENT SLOUGH – EXCISING THE ABSCESS
HOT ABSCESS – SURGERY RARE
HANDS
SPECIAL CARE WHEN WORKING WITH HANDS OR COOKING MEALS
NEVER PICK UP A PAN OR OTHER OBJECT THAT MIGHT BE HOT, WITHOUT FIRST PROTECTING HAND WITH A THICK GLOVE OR FOLDED CLOTH
AVOID WORK THAT INVOLVES HANDLING SHARP OR HOT OBJECTS.
DO NOT SMOKE
USE TOOLS WITH SMOOTH, WIDE HANDLES, OR WRAP CLOTH AROUND HANDLES
FOR A PERSON WITH WEAK OR DEFORMED FINGERS - HOLD A TOOL OR UTENSIL - YOU CAN MOLD HANDLE TO THE SHAPE OF THE PERSON’S CLOSED HAND.
FEET
AVOID GOING BAREFOOT. USE SHOES OR SANDALS
LEARN TO TAKE SHORT STEPS
INJURY CAREEYES –
CLOSE EYES OFTEN. IF NECESSARY USE A SIMPLE EYE PATCH
IF EYE GETS INFECTED - ANTIBIOTIC EYE OINTMENT- LOWER LID WITHOUT TOUCHING THE EYE
HANDS AND FEET
IF YOU HAVE A CUT OR SORE, KEEP THE INJURED PART VERY CLEAN AND AT REST UNTIL IT HAS HEALED COMPLETELY
TAKE CARE NOT TO INJURE THE AREA AGAIN
THINGS TO DO EVERY DAY EXAMINE HANDS AND FEET CAREFULLY OR
SOMEONE ELSE EXAMINE THEM. LOOK FOR CUTS, BRUISES THORNS, SPOTS
OR AREAS ON THE HANDS AND FEET THAT ARE RED, HOT, SWOLLEN OR SHOW THE START OF BLISTERS
IF YOU FIND ANY OF THESE – REST THE HANDS OR FEET - SKIN IS COMPLETELY NORMAL AGAIN
IF THE SKIN GETS DRY AND CRACKS - SOAK FEET DAILY - WATER - 20 MIN
THEN RUB COOKING OIL, VASELINE, OR LANOLIN HAND CREAM INTO THEM
DO STRETCHING EXERCISES - KEEP COMPLETE RANGE OF MOTION IN THE JOINTS
CONTINUED DAILY CARE, MOST DEFORMITIES OF LEPROSY CAN BE PREVENTED
PREVENTION OF CONTRACTURES AND DEFORMITIES
EYE
HANDLOSS OF FEELING MAKES
PREVENTION MORE DIFFICULTEXERCISES TO PREVENT FIXED
CLAWING OF THE HANDS CAN BE DONE BY GENTLY STRAIGHTENING THE FINGERS
SPLINTAGE
NERVE INJURED SPLINT USED
RADIAL NERVE PALSY COCK-UP SPLINT
ULNAR NERVE PALSY KNUCKLE BENDER SPLINT
COMMON PERONEAL NERVE INVOLVEMENT
FOOT DROP SPLINT
COCK - UP SPLINT
KNUCKLE BENDER SPLINT
FOOT DROP SPLINT
GOOD EXERCISE TO PREVENT ‘TIPTOE’ CONTRACTURES WITH ‘FOOT DROP’ IS TO STRETCH THE HEEL CORDS BY LEANING FORWARD AGAINST A WALL OR BY SQUATTING WITH HEELS ON THE GROUND
FOOT WEAR USED IN LEPROSY
WELL – FITTED UPPER PART THAT DOES NOT RUB AND HAS PLENTY OF TOE ROOM
A SOFT INNERSOLE ABOUT 1 CM THICK
A TOUGH UNDER-SOLE, SO THORNS, NAILS AND SHARP ROCKS DONOT INJURE FOOT
FOOTWEAR SHOULD BE ACCEPTABLE AND NOT LOOK STRANGE SO THAT THE PERSON WILL USE IT
THINGS TO BE AVOIDED
PLASTIC SHOES OR SANDALSSOFT-SOLED SANDALS OR THONGS
THAT THORNS CAN PASS THROUGH
USING NAILS TO FASTEN HEELS AND SOLES
POSSIBLE WAYS TO GET FOOTWEAR
CONTACT A LEPROSY HOSPITAL WITH A FOOTWEAR WORKSHOP. THEY CAN MAKE SANDALS IF YOU SEND A TRACING OF THE FOOT
CHECK THE MARKET. YOU MAY FIND A CANVAS SHOE OR TENNIS SHOE THAT ALREADY HAS A GOOD INSOLE
OR THEY CAN PUT SOFT INSOLES INTO THE SHOES
MAKE SPECIAL FOOTWEAR. FOR THE INNER SOLE, YOU CAN USE A SOFT SPONGE SANDAL OR THONG OR BUY MICROCELL RUBBER WHICH IS SOFT BUT FIRM.
FOR THE UNDER SOLE YOU CAN USE A PIECE OF OLD CAR TIRE.
FOR PERSONS WHO HAVE DEVELOPED SORE ON THEIR FOOT - FOOT SUPPORT HERE MAY HELP TAKE PRESSURE OFF THE BALL OF THE FOOT AND PREVENT NEW SORES.
TO PREVENT SORES – A SOFT, HEAT-MOLDABLE FOAM PLASTIC CALLED ‘PLASTAZOTE’.
LACES SHOULD BE AVOIDED. IN THAT CASE VELCRO IS AN IDEAL ALTERNATIVE
FOR PERSONS WITH A ‘DROP FOOT’, A BRACE OR LIFT CAN HELP PREVENT SORES AND INJURIES
GET A BRACE OR SUPPORT AT A REHABILITATION WORKSHOP OR MAKE A SPECIALLY-FITTED, WELL-PADDED PLASTIC BRACE
MAKE A SIMPLE DEIVICE TO HOLD THE FOOT UP
ORTHOPAEDIC SURGERY AND PLASTIC SURGERY
PARALYSED FINGERS – STRAIGHTENED BY TAILED GRAFT OF BRAND - PLANTARIS TENDON
DROPPED FOOT – TRANSVERSE TIBIALIS POSTERIOR MUSCLE
CLAWED HAND AND TOES – TRIPLE ARTHRODESIS
CHRONIC PLANTAR ULCERATION – REMOVAL OF DAMAGED META-TARSAL WITH EXCISION OF THE ULCER
GROSS DEFORMITY OR BONE DESTRUCTION – BELOW KNEE AMPUTATION
WHEN TREATMENT IS COMPLETED CONGRATULATE THE PATIENT
THANK FAMILY / FRIENDS FOR THEIR SUPPORT REASSURE THAT MDT COMPLETELY CURES
LEPROSY ANY RESIDUAL LESIONS WILL FADE AWAY
SLOWLY SHOW THEM HOW TO PROTECT ANAESTHETIC
AREAS / DISABILITIES ENCOURAGE TO COME BACK IN CASE OF ANY
PROBLEM TELL THAT THEY ARE WELCOME TO BRING
OTHER MEMBERS OF FAMILY OR FRIENDS FOR CONSULTATION
REMOVE THE PATIENT’S NAME FROM THE TREATMENT REGISTER
BIBLIOGRAPHY
JOPLINGHASTINGSPARK MAHESHWARI SNELL’S CLINICAL ANATOMY INTERNET