Is It Cystic Fibrosis?Identifying Patients With Atypical CF

The Changing Epidemiology of CF

The Changing Epidemiology of CF (cont)

Organ System Involvement in “Classic” CF

Criteria for CF Diagnosis

Sweat Chloride Test Results in Patients With CF

European CF Diagnostic Criteria

Pancreatic Sufficiency and Residual Function Mutations

The Continuum of Pancreatic Sufficiency and Genetic Mutations

Clinical Presentation

Adult Diagnosis of CF Is Associated With Milder Lung Disease

Incidence of CFTR Mutations in Patients With Idiopathic

Pancreatitis

CBAVD

Clinical Implications of Carrying a 5T Mutation Trans to a Classic CF Mutation

Clinical Implications of the R117H Mutationa-d

CFTR Spectruma-e

CF Diagnostic Categoriesa,b

CFTR2 Classification of Mutationsa

When to Suspect CF

When to Suspect CF (cont)

Location of Bronchiectasis Can Provide a Clue to the Diagnosis

What to Do if You Suspect CF

Abbreviations

References

References (cont)

References (cont)