Abstracts 1827

Gingival ameloblastic fibro-dentinoma–—Report of a case in a child

Hong-Sen Chen a, Wen-Chen Wang b, Yu-JuLin b, Yuk-Kwan Chen b,*, Li-Min Lin b,*aDepartment of Pediatric Dentistry, School ofDentistry, Kaohsiung Medical University, 100,Shih-Chuan 1st Road, Kaohsiung, TaiwanbDepartment of Oral Pathology, School of Dentis-try, Kaohsiung Medical University, 100, Shih-Chuan1st Road, Kaohsiung, Taiwan

Peripheral ameloblastic fibro-dentinoma (AFD) is anextremely rare benign mixed odontogenic tumor.From a review of the English-language literature, tothe best of our knowledge only two gingival caseshave previously been reported. Here, we report aninteresting case of AFD occurring in the upper labialgingiva between the central incisors of a child, inorder to raise awareness of the possible presence ofthis pathologic entity.

DOI: 10.1016/j.ijporl.2005.11.018

Sudden sensorineural hearing loss aspresenting symptom of multiple sclerosisin a 15-year-old girl

G. Cadoni *, S. Agostino, S. Scipione,A. CianfoniDepartments of Otorhinolaryngology and Radiol-ogy, Catholic University of the S. Heart,Largo A. Gemelli 8, 00168 Rome, Italy

Multiple sclerosis (MS), a chronic inflammatory dis-order of the central nervous system results indamage to axons and their surrounding myelinsheath. Sensorineural hearing loss (SNHL) is anuncommon symptom of MS. We describe the caseof a 15-year-old girl with unilateral sudden hearingloss as presenting symptom of multiple sclerosis.

DOI: 10.1016/j.ijporl.2005.11.019

Giant tonsillolith in a child

Joginder Singh Gulia a,*, Virender Singh b,Samar Pal Singh Yadav a, Anita Hooda c

a Department of Otorhinolaryngology, Pt. B.D.Sharma PGIMS, Rohtak, Haryana, IndiabDepartment of Oral Surgery, Pt. B.D. SharmaPGIMS, Rohtak, Haryana, IndiacDepartment of Oral Anatomy, Pt. B.D. SharmaPGIMS, Rohtak, Haryana, India

Tonsilloliths are calcifications that form in the cryptsof the palatine tonsils. These are usually seen inadults but are uncommon in children. A case witha large tonsillolith measuring 35 mm � 22 mm �22 mm in a child is presented, which is the largestreported in pediatric age group. Surgical treatmentand sometimes-even tonsillectomy may be neededin such a large tonsillolith.

DOI: 10.1016/j.ijporl.2005.11.020

Posttransplantation lymphoproliferativedisorder of the paranasal sinuses in achild

Frederick S. Rosen a,*, David Bingham b,Kay W. Chang a

aDepartment of Otolaryngology — Head and NeckSurgery, Lucile Packard Children’s Hospital/Stan-ford University Medical Center, 801 Welch Road,Route 5739, Palo Alto, CA 94304, USAbDepartment of Pathology, 300 Pasteur Drive, Lane235, Stanford, CA 94305-5324, USA

Posttransplantation lymphoproliferative disorder(PTLD) represents an often fatal complication ofchronic immunosuppression following solid organor bone marrow transplantation. PTLD in the headand neck is uncommon and generally involves lym-phoproliferation in Waldeyer’s ring, cervical lym-phadenopathy, or both. This unusual case of PTLDinvolving the paranasal sinuses in a child illustratesthe difficulty in distinguishing PTLD from invasivefungal sinusitis. Promptly establishing the correctdiagnosis via biopsy is critical to the successfulmanagement of such a patient.

DOI: 10.1016/j.ijporl.2005.11.021

Maxillar localization of a congenitalperipheral primitive neuroectodermaltumorA case report

C. Martins Carvalho, G. Valette, G. Nicolas,C. Fortun, R. Marianowski *Department of Oto-Rhino-Laryngology, CHU A.Morvan, Avenue Marechal Foch, 29200 Brest, France

Peripheral primitive neuroectodermal tumor is veryrare in children and congenital forms are excep-tional. This tumor belongs to the Ewing’s sarcoma

1828 Abstracts

(ES) family and the difficulty of diagnosis lies in theconfusion with rhabdomyosarcoma, neuroblastoma,ES and lymphoma. Diagnosis is only performed byimmunohistochemistry and RNA analysis. Congenitalperipheral primitive neuroectodermal tumor seemsto be more aggressive and refractory to treatmentthan non-congenital forms. In literature,most of thepatients die within 6 months of diagnosis despitetherapy. We report the first case of congenital per-ipheral primitive neuroectodermal tumor localizedin the left maxillary bone of a full-term femaleinfant.

DOI: 10.1016/j.ijporl.2005.11.022

Unusual cause for unilateral nasalobstruction in a child

Boggaram R. Girish *, Indira NarsimhanDepartment of E.N.T. and Head and Neck, SriDevraj Urs Medical College, India

An unusual presentation of a common anatomicalvariation presenting as unilateral nasal obstructionin a child of 14 years. Choncha bullosa is a commonanatomic variant seen in 34—53%; it can be thecause of the osteomeatal obstruction predisposingto sinusitis and their complications due to mucosalcontact points and impairing the mucociliary clear-ance or causing mechanical obstruction at theosteomeatal complex. Here we are presenting acase of unusually large concha bullosa, which wascausing unilateral nasal obstruction, deviated sep-tum and bilateral anterior sinusitis and recurrentchest infection in a 14-year-old girl. The conchabullosa was filled with thick pus making it apyocele. The culture did not grow any organisms.The CT scan done was not conclusive the origin ofthe lesion but could be diagnosed only during thesurgery.

DOI: 10.1016/j.ijporl.2005.11.023

Postcricoid inflammatory myofibroblastictumor (inflammatory pseudotumor) in a10-year-old girl

Nathan B. Sautter *, Paul R. Krakovitz,Erinn Downs-Kelly, Peter J. KoltaiCleveland Clinic Foundation, Head and Neck Insti-tute, 9500 Euclid Avenue, 44195 Cleveland, OH,USA

Inflammatory myofibroblastic tumor (IMT) is abenign spindle cell tumor of disputed nosologyand unknown etiology that occasionally presentsin the head and neck but is known to occur through-out the body in patients of all ages. IMT is identifiedby several alternative names in the literature;inflammatory pseudotumor and plasma cell granu-loma are among the most prominent. We present acase of IMT arising in the postcricoid region of thehypopharynx in a 10-year-old girl and review theliterature of IMT involving the head and neck. Tothe best of our knowledge, this is the first report ofan IMT arising in this location. The patient wastreated with endoscopic surgical excision andremains free of disease 2 years following the initialsurgical resection. Histologically, the differentialdiagnosis of IMT includes both benign and malig-nant neoplasms, making frozen section interpreta-tion challenging. Highlighting this is a case reportwherein the presumptive frozen section diagnosiswas interpreted as rhabdomyosarcoma, whilepermanent histology was consistent with IMT.Therefore, surgical decisions based purely on afrozen section diagnosis of malignancy may resultin inappropriate and overly aggressive surgicaltreatment.

DOI: 10.1016/j.ijporl.2005.12.022

Transnasal endoscopic marsupializationfor a large midline maxillary odontogenickeratocyst in a 6-year-old child

Yuh-Chyun Chiang a,c, Pin-Zhir Chao b,c,Tsung-Han Yang b,c, Bou-Yue Peng d,Fei-Peng Lee b,c,*aDepartment of Otolaryngology, Taiwan AdventistHospital, No. 424, Pa Te Road, Section 2, Taipei,TaiwanbDepartment of Otolaryngology, Taipei MedicalUniversity Hospital, No. 252, Wu-Hsing Street,Taipei, TaiwancDepartment of Otolaryngology, Taipei MedicalUniversity, No. 250, Wu-Hsing Street, Taipei, TaiwandDental Department, Taipei Medical UniversityHospital, No. 252, Wu-Hsing Street, Taipei, Taiwan

An odontogenic keratocyst is a histologicallydistinct lesion that is thought to arise from basalcells of the oral epithelium, usually occurring inthe posterior portion of the mandible or the man-dibular ramus. We report on a large odontogenickeratocyst that presented as nasal airway obstruc-tion in a 6-year-old boy. To our knowledge, this is