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Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez, Cecilia Ridaura, Florian Nagl, Marimar Sáez-de- Ocariz, Carola Durán-McKinster, Ramon Ruiz-Maldonado, Georgia Alderete, Peter Grube, Carmen Lome-Maldonado, Irina Bonzheim, and Falko Fend Blood Volume 122(18):3101-3110 October 31, 2013 ©2013 by American Society of Hematology

Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

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Page 1: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

Hydroa vacciniforme-like lymphoma: a chronic EBV+ lymphoproliferative disorder with risk to develop a

systemic lymphoma

by Leticia Quintanilla-Martinez, Cecilia Ridaura, Florian Nagl, Marimar Sáez-de-Ocariz, Carola Durán-McKinster, Ramon Ruiz-Maldonado, Georgia Alderete, Peter

Grube, Carmen Lome-Maldonado, Irina Bonzheim, and Falko Fend

BloodVolume 122(18):3101-3110

October 31, 2013

©2013 by American Society of Hematology

Page 2: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

Skin lesions in HVLL. (A-B) Multiple skin lesions in face and ear lobes characterized by vesicles, erythema, and crusts.

Leticia Quintanilla-Martinez et al. Blood 2013;122:3101-3110

©2013 by American Society of Hematology

Page 3: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

HVLL morphology and immunophenotype.

Leticia Quintanilla-Martinez et al. Blood 2013;122:3101-3110

©2013 by American Society of Hematology

Page 4: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

Immunohistochemical analysis, EBER ISH, and molecular analysis in a case with γδ T-cell phenotype (case 6).

Leticia Quintanilla-Martinez et al. Blood 2013;122:3101-3110

©2013 by American Society of Hematology

Page 5: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

Immunohistochemical analysis and EBER ISH in a case with NK-cell phenotype (case 15).

Leticia Quintanilla-Martinez et al. Blood 2013;122:3101-3110

©2013 by American Society of Hematology

Page 6: Hydroa vacciniforme-like lymphoma: a chronic EBV + lymphoproliferative disorder with risk to develop a systemic lymphoma by Leticia Quintanilla-Martinez,

Morphology and comparative TCR-γ clonality analysis in case 4.

Leticia Quintanilla-Martinez et al. Blood 2013;122:3101-3110

©2013 by American Society of Hematology