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7/24/2019 Congenital Abnormalities (2)
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CONGENITAL ABNORMALITIES
OF GENITALIA MALE
Oleh :
Dr. Bakri B. Hasbulloh, SB.FINACS
Ba!ia" Be#ah F$ %MS& RS%D $ab.$ara"!a"'ar
Se"i" : () Ok*ober +))
S%RA$ARTA
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PATHOLOGY OF DISEASE :
CONGENITAL
TRAUMA
INFECTION
DEGENERATIVE
/ METABOLISMCANCER
SURGERY INTERNIS PEDIATRIC
OBGYNE / GYNECOLOGY THT
SYARAF
KULIT KELAMIN MATA
RADIOLOGY PULMONOLOGY
RM REPRODUCTIVE
Dll.
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FE"TILITY #$ I%FE"TILITY :
CONGENITAL
TRAUMA
INFECTION
DEGENERATIVE
/ METABOLISMCANCER
COUPLE (PASANGAN SUAMI-ISTRI) CINTA ANAK FERTILE
INFERTILE : AFTER MARRIED 1- YEARS NO CONTRACEPTION NORMAL SE!UAL NO BABY
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I%FE"TILITY :
pre testiculer
testiculer
post testiculer
H"#$%&l&' *"#$+,
%,%"
#,"
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Keli!! p" #ipot#l$us
D,,"," LH FSH &%& GRH Keli!! p" #ipo%se
I+"," *"#$+" $/0 %'$ &2"&"$#,&"
Keli!! p" testiculer A$'&l" K$'$$' A$3*"' 4"l&%,&l G$&2$%$0" : ',0&
#,'&%$5,," T&'& %,%" P,6&0"% "%,'"0 # DM. *"#,%," 2ll V&"0$0,l K"#%$3*"'
K,l&"& #&3& %,%"0l, G&55& %$% #,'& : CBAVD K,l.5" 2& %'$%"l"%& #,'&
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EMBR-OLOG- OF HE MALE
ETERNAL GENITALIA
NORMAL DEVELOPMENT : AT THE END of 2 weeks of development2 cell
layes :
T!e ectodem
T!e P"m"t"ve #teak T!e Entodem
$ T!e %loacal Mem&an $ T!e Alanto"s
THE ME#ODERM
$ T!e e'tenal (en"tal"a and an)s ae fomed &y developments
a&o)t t!e cloacal mem&an and t!e allanto"s
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Ab"or/ali*i*ies
H*PO#PAD+A# AND %HORDAET!e )et!al meat)sOn t!e vental s)face of t! s!aft
of t!e pen"s
A laye of f"&o)s t"ss)e%HORDAE
EP+#PAD+A# AND E,TROPH*
T!e )et!al meat)s On t!e dosal s)face of t! s!aftof t!e pen"s
T!e mem&ane ves"ca )"na"a defectE,TROPH*
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A!to$il&0"
1.ORGAN T,%" :
T,%$%,$ S#,'&%$7$&
E#"2"2"'" V&2,,, V,"3l& ,'"&l" P,"
.PROSESSPERMATOGENESIS T4l
,'"",
8.HORMON T,%$%,$
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&I'OS'ADIA
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&iposp"i !terior tipecoro!l
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Masalah Hiosa#ia
C%ASA : M%LTIFACTORIAL -enet"k
Homonal
Ras dll
RE0ROD%$SI Pancaan spemato.oa
SE$S%AL Pa"n
%ROLOGI #tenos"s
#t"ct)e
#tone
+#/ 0"nfeks" sal)an kenc"n(1
URETHRA LETAK DI
SEPAN9ANG PENISBUKAN DI TOPGLAND PENIS
PANCARANABNORMAL
PENIS MELENGKUNG DAN
PENDEK
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TI0E HI0OS0ADIA
acat 034561 &edasakan letak ost")m )et!aekstena te&a(" 7 t"pe : T"pe (land
Pat Ante"o
8795;
T"pe coonal
T"pe pen"lPat Pen"l 3937;
T"pe penoscotal
Pat Poste"o
2;
T"pe pe"neal
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THERA0-
%HORDE%TOM* Meelease c!odaePen"s
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1 0er*i/ba"!a" 0re Oera*i2e
1. USIA Usi ( )ul! s$pi usi se)elu$ se*ol#
+, TI'E &I'OS'ADIA-,
BESAR 'ENIS., ADA TIDAKNA C&ORDAE
BERHUBUNGAN
DENGAN ONESTAGE OR TO
STAGE OPERATIVE
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COM'LICATION
AERLY :BLEEDING
INFECTION
OEDEMA
LATEFISTULE URETHRACUTANEUS
REST CHORDAE
STRICTURE URETHRAE
STENOSIS URETHRAE
DIVERTICLE URETHRAE
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'ROGNOSIS
COMMONL- : BAI$
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3ASSALAAM%4ALAI$%M
33
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