refrat hiperbilirubin

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    REFERAT

    HIPERBILIRUBINEMIA

    Disusun oleh:

    Fiki Setiawan 1102012086

    Pembimbing:

    dr. Pulung M Silalahi Sp. A

    KEPANITERAAN KLINIK ILMU KESEHATAN ANAK

    RUMAH SAKIT BHAYANGKARA TK I RADEN SAID SUKANT!

    FAKULTAS KED!KTERAN UNI"ERSITAS YARSI

    1

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    KATA PENGANTAR

    Puji serta syukur kita ucapkan kepada Allah SW atas selesainya re!erat

    yang "erjudul #iper"iliru"ine$ia. %epada dr. Pulung M Silalahi SP.A selaku d&sen

    pe$"i$"ing' saya juga ucapkan teri$a kasih "anyak atas "i$"ingannya sela$a

    kepaniteraan ka$i di (agian )l$u %esehatan Anak *.S (hayangkara ingkat )

    *aden Said Sukant&.

    +ala$ re!erat ini ka$i akan $enc&"a $e$"ahas $engenai

    #iper"iliru"ine$ia. Se$&ga pe$"ahasan ka$i ini dapat $e$"antu $e$"uka

    wawasan dan pengetahuan "agi $ahasiswa klinik ataupun d&kter u$u$

    $engenai #iper"iliru"ine$ia.

    Penulis'

    ,akarta' ,uni 2016

    2

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    DAFTAR ISI

    KATA PENGANTAR...............................................................................................2

    DAFTAR ISI............................................................................................................3

    BAB I

    LATAR BELAKANG..............................................................................................4

    BAB II

    TINJAUAN PUSTAKA.............................................................................................

    2.2 ETIOLOGI....................................................................................................7

    2.3 METABOLISME BILIRUBIN.....................................................................8

    2.4 HIPERBILIRUBINEMIA...........................................................................11

    2.5 PENYEBAB IKTERUS..............................................................................15

    2.6 KLASIFIKASI............................................................................................17

    2.7 MANIFESTASI KLINIS.............................................................................18

    2.8 TATALAKSANA........................................................................................19

    2.9 TRANFUSI TUKAR...................................................................................24

    BAB III

    KESIMPULAN......................................................................................................26

    DAFTAR PUSTAKA.............................................................................................27

    -

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    BAB I

    PENDAHULUAN

    1.1. L!" B#$%&'

    T(# )*"$+ H#$!( R#,*"! 2--8 #&'!%& /(0 AKB + I&+* #&,

    2-1--- %#$("& (+, SDKI 2--72--8. B#""! #!, !#"+,! 1- / /" $("

    #&&''$: #!, (" + 246 / #&&''$ +& #!, !(& + 89.77- / /"

    $(" &' #&&''$. K#!& / $(" #/#" 79; !#"+ #!, &'' ,#"!

    %#$("& !#"! ,+ ! ,#"$&&. S#/&% 54; !#"+ ,+ !&'%!& %#$"'

    &' #/'& /#" +#//%& !+% #,#"*$#( $&& "%& +& %"&'&

    ,#&'#!(& %#$"' %& %#'0!+""!& ,+ /. P#// ! %#!& /

    /" $(" +$( ,"#!"!: BBLR: 5 '+L +#/! +#&'& (,#"/$"/.

    H,#"/$"/ & &*"$: (& 1-; &' /#",*!#& #&+ ,!*$*'

    # 2 '+ ! > 2- ;

    +" BST.

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    H,#"/$"/ ++#

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    2.1. D#

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    G/" 2.1 %+" #" /$"/& N*"*'" B(!&

    2.2. E!*$*'

    P#// %!#" ,+ / $(" +,! /#"+" #&+" !,& +,! +#//%& *$#(

    /#/#",

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    $& $( +#

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    & !+% $"! +$ " +& %#+& %& +!"&,*"!%& %# #$ (#,". B$"/& &'

    !#"%! ,+ $/& /#"

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    B$"/& &' !% !#"%*&' +%*C#"%& %# /#&!% /$"/& %*&' &' $"!

    +$ " +"#!%$ #&+*,$ +#&'& /&!& # uridine diphospate glucoronosyl

    transferase UDPGT. B$"/& & %#+& +#%%"%& %# +$ %&$%$ #,#+.

    S#+&'% ! *$#%$ /$"/& &' !% !#"%*&' %& %#/$ %# "#!%$

    #&+*,$!% &!% "#%*&' /#"%!&.

    S#!#$( #&'$ ,"*# %*&': /$"/& %& +#%%"#%& %# +$ %&+&'

    #,#+: %#+& #% $"& #"& +& +#%"#%& #$$

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    /$&: +& / &' #&+#%! %, /$&. N#*&!$ (,#"/$"/ !#"+ %"#&

    ,#&'%!& ,"*+% ! ,#&"&& clearance /$"/& +& $#/( #"&' !#"+ ,+ /

    !".

    H,#"/$"/ &' '&

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    P#&%! (#*$!% ! ,#&&'%!& %##,!& +#!"% #$ +"( #",%&

    ,#// ! +" ,#/#&!%& /$"/& &' /#"$#/(&. I%!#" &' !/$

    #"&' +#/! %!#" (#*$!%. K*&' +& !"&

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    H,#"/$" !% !#"%*&' &' "&'& 12:91-- $ &' $

    !#"+ ,+ (" %# + , %#$ #!#$( $(" +#/! %!#"

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    +%/!%& *$#( (,#"/$"/ !#"%*&' /& $#/( %&&'

    +/&+&'% +#&'& (,#"/$"/ !% !#"%*&'.,#"/(& 0"& /#"%"

    +" %&&' &'' + ! , %&&' ( /$ !#"+ */!"% !*!$

    $"& #,#+ ,#"/(& & #",%& /%! +& %!#" %*$#!!%: &'

    #",%& & $& +" %!#" */!"%!

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    $"& ,#"&&: #(&'' %& ++,!%& ,#&&'%!& %+" "*/$&*'#& ++$

    !&.

    P#&'%!& %+" /$"/& +,! +#//%& *$#( ?

    1. K#$&& ,+ #$ +"( #"(2. I% #,#"! $": #,

    3. T*%& &' /#"$ +" $" !/( #,#"! */! */!&: ,& &' /#"$ +"

    +$ !/( #,#"! &' !#"+ ,+ "#% !"&

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    (#,!% ,/$ ,#&/!& !#"+ + &!" (#,!*! +& +%! %*$#+%!: +&

    #%!"(#,!% /$ /!& !#"+ ++$ +%! %*$#+%!.

    2.6. %$

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    D#"! (,#"/$"/ #&"! %"#"

    2.7. &

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    &' +!&+ *$#( +#,* ,'#& /$"/& ,+ /#/#", +#"( + *!% !#"! +

    '&''$ /$:,*&: +& #"#/#$. M&

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    . I&*'$*/$& &!"C#& !#$( +'&%& ,+ / / +#&'& "(# &' /#"!

    +& &%*,!/$! ABO &!% #%& (#*$ *& +& #"&%& !&+%&

    !"&

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    S&"

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    ,#"%& !/( &' !#",,". I&!#&! &' +/#"%& #&!%& #

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    #&&'%!& /$"/& &+"#% ,+ . P##/#"& +#&'& %+" $%!*

    "#&+( %& #&'"&' !/$& +"#.

    3. T/$& %#$&& %$! &' #"&' +#/!flea ite rash++#"( %: /+&

    +& #%!"#!. K#$&& & #'#" ($&' #!#$( !#", +(#&!%&. P+

    /#/#", / +$,*"%& ,$ %#&'%&& !#"+ /"*#& // &+"*#. H$

    & !#"+ %"#& !/( !+% , #&'#$"%& +#&'& #'#" ($ !#",

    &". P#/(& 0"& %$! &' /#"

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    &!/*+ !#"&$ +" "%$ /. S#(&'' #'( (#*$ $#/( $&! +&

    #,#"/% .

    1. I&+% !"&

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    BAB III

    KESIMPULAN

    P+ / /" $(" !#"! ,+ / +#&'& /#"! /+& $(" "#&+( ! /

    ,"#!" #&'$ %!#" ,+ &'' ,#"! %#(+,&. D" +! #,+#*$*' /(0

    5-; / /" $(" #&+#"! %!#" +,! ++#!#% ,+ &'' ,#"! %#(+,&.

    I%!#" +$( 0"& %$!: %* +& %$#" #&+ %&' %"#& ,#&&'%!& %+"

    /$"/& +"( #&&'%!. I%!#" +,! #&+

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    DAFTAR PUSTAKA

    1. B% A" N#*&!*$*' I%!& D*%!#" A&% I&+* E+ P#"! 2--8: FKUI ?

    J%"!

    2. P"#: S$C M. )$*& L*"". P!*